Left pulmonary artery originating from the right coronary artery in a patient with pulmonary atresia and ventricular septal defect.

We describe a patient with pulmonary atresia and ventricular septal defect in whom the left pulmonary artery was originating from the dilated right coronary artery. Successful division of the left pulmonary artery from the right coronary artery and the connection with the right ventricular outflow tract was carried out with closure of the end of the origin. The preoperative accurate diagnosis of this anomaly with ascending aortography is the most important in the surgical management of patients with pulmonary atresia and ventricular septal defect.