A case of prune belly syndrome.

Journal: Pediatrics And Neonatology
Published:
Abstract

Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, "prune-like" abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery-right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection.

Authors
Wei Xu, Hui Wu, Dong-xuan Wang, Zhi-hong Mu
Relevant Conditions

Prune Belly Syndrome