Systemic panniculitis-like T-cell lymphoma with involvement of mesenteric fat and subcutis.
Journal: Journal Of Cutaneous Pathology
Published:
Abstract
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is an uncommon non-Hodgkins primary cutaneous lymphoma that typically presents as subcutaneous nodules on the extremities or trunk. Here, we report an unusual case of systemic panniculitic T-cell lymphoma with predominantly mesenteric extra-cutaneous involvement and an aggressive clinical course with histopathologic and immunophenotypic features that mimic SPTCL. This case serves to expand the body of literature regarding systemic SPTCL-like disorders with prominent extra-cutaneous involvement.
Authors
Laura Lester, Mark Ewalt, Roger Warnke, Jinah Kim
Relevant Conditions