Redo Valve-Sparing Root Replacement for Delayed Cusp Derangement From Ventricular Septal Defect.

A 28-year-old man with ventricular septal defect, double-chambered right ventricle with associated right ventricular outflow tract obstruction, and anomalous right coronary artery underwent resection of the double-chambered right ventricle, transaortic ventricular septal defect repair, and unroofing of anomalous right coronary artery. Two years later, he returned with delayed presentation of ventricular septal defect flow funnel-related aortic cusp prolapse and symptomatic severe aortic regurgitation. He underwent reoperative valve-sparing aortic root replacement and aortic cusp repair with an excellent outcome.