Echocardiographic diagnosis of Shone's syndrome.
Journal: Echocardiography (Mount Kisco, N.Y.)
Published:
Abstract
Shone's syndrome is a rare congenital heart disease that includes 4 cardiovascular anomalies: supravalvular mitral ring, parachute mitral valve, subaortic stenosis, and coarctation of the aorta. Early diagnosis and treatment result in better outcomes. Echocardiography plays an important role in the diagnosis and is the optimal examination for detecting this disease. Pressure gradients are often unreliable and inaccurate; thus, careful anatomical observation of the left ventricular inflow and outflow tracts, particularly the mitral valve, is vital for accurate diagnosis and planning appropriate management. Herein, we describe 9 cases of Shone's syndrome, diagnosed with echocardiography and treated surgically.
Authors
Xin Zhang, Guiqin Ma, Lin Zheng, Hongju Zhang, Yan Sun, Jingya Li, Ning Ma
Relevant Conditions