Background: Intestinal atresia more common in the small bowel, apart from large intestine. Jejunal atresia characterized by complete occlusion of the intestinal lumen, is a rare congenital anomaly occurring in 1 in 12,000 live births.

Objective: The jejunal atresia can be single or multiple occurring anywhere from the ligament of Treitz to the jejuno-ileal junction, requiring immediate surgical attention to prevent mortality and morbidity among these neonates.

Methods: A rare case of jejunal atresia in neonate and its management has been discussed here. Surgical excision of the involved bowel and end to end anastomosis of the normal bowel is definitive treatment.

Conclusions: The morbidity associated with post-operative hypo persistaltic bowel can be minimised by adding oral prokinetics in controlled manner.