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Autoimmune Pancreatitis: A Review.

Journal: Journal Of Clinical Medicine
Published: March 18, 2025
Abstract

Autoimmune pancreatitis is a rare condition of pancreatic inflammation with two classic subtypes. The emergence of a third subtype, ICI-induced pancreatitis, highlights the need for knowledge of each type to ensure accurate diagnosis and treatment. Abbreviations: AIP-Autoimmune pancreatitis; AIP-1-Type 1 autoimmune pancreatitis, also known as lymphoplasmacytic sclerosing pancreatitis (LPSP); AIP-2-Type 2 autoimmune pancreatitis, also referred to as idiopathic duct-centric pancreatitis (IDCP); AIP-3-Type 3 autoimmune pancreatitis, also known as immune checkpoint inhibitor (ICI)-induced autoimmune pancreatitis; IgG4-RD-Immunoglobulin G4-related disease.

Authors
Varun Vemulapalli, Cristina Natha, Anusha Shirwaikar Thomas
Relevant Conditions

IgG4-Related Disease, Hereditary Pancreatitis

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