Here, we reviewed the skin diseases with ulcerative colitis. The cutaneous manifestations were divided 7 groups; 1) pyoderma gangrenosum (PG), 2) erythema nodosum (EN), 3) acneiform eruption, 4) aphtha, 5) bullous diseases (Bullous pemphigoid, Linear IgA bullous dermatosis), 6) urticarial vasculitis, 7) pyostomatitis vegetans. Most of these skin manifestations were occurred after the onset of UC. These were commonly parallel with the clinical course of UC. The pathomechanisms of the cutaneous alterations have not been fully understood. However, these signs seen in the UC patients were important for the evaluations of disease activity of UC.